Variable | Healthy | DMD Brooke 1 | DMD Brooke 2 | DMD Brooke 3 | DMD Brooke 4 | DMD Brooke 5 |
---|---|---|---|---|---|---|
N | 20 | 5 | 8 | 4 | 3 | 3 |
Age (median, range) | 14.0 (7.4–23.4) | 11.1 (8.0–16.0) | 12.4 (8.7–15.8) | 15.8 (12.6–16.9) | 17.1 (17.0–18.4) | 18.2 (17.8–21.7) |
BMI | 19.1 (15.7–24.4) | 21.9 (17.7–26.4) | 20.7 (18.7–30.8) | 23.0 (16.5–26.0) | 17.6 (10.0–21.4) | 22.5 (19.4–24.6) |
Hand preference | ||||||
Right handed (%) | 90 | 100 | 87.5 | 75 | 100 | 100 |
Left handed (%) | 10 | 0 | 12.5 | 25 | 0 | 0 |
Age of diagnosis (median, range) | - | 2.0 (0.0–5.0) | 4.0 (2.5–7.0) | 4.0 (2.5–6.0) | 1.5 (0.0–6.0) | 1.0 (0.0–6.0) |
Percentage wheelchair confined (%) | - | 0 | 87.5 | 100 | 100 | 100 |
Age wheelchair confined (median, range) | - | - | 10 (7–13) | 10 (8–10) | 11 (10–11) | 9 (8–10) |
Scoliosis | ||||||
No (%) | - | 75 | 87.5 | 75 | 33 | 0 |
Mild (%) | - | 25 | 12.5 | 0 | 0 | 33 |
Severe (%) | - | 25 | 67 | 67 | ||
Scoliosis correction (%) | - | 0 | 0 | 0 | 33 | 67 |
Corticosteroid use | ||||||
No (%) | - | 0 | 12.5 | 25 | 33 | 0 |
Not anymore (%) | - | 0 | 0 | 25 | 0 | 67 |
Yes (%) | - | 100 | 87.5 | 50 | 67 | 33 |